VATER ASSOCIATION: A CASE REPORT

Kural N¹, Dinleyici EC¹, Ilhan H², Kaya T³

Department of Pediatric Nephrology¹, Pediatric Surgery² and Radiology³,

Osmangazi University Faculty of Medicine, Eskisehir, Turkey

VATER association is clinical entities which includes vertebral defects, anal atresia, tracheooesophageal fistula with atresia, renal anomalies and radial upper limb dysplasia. In this report a ten-year-old boy who was diagnosed as VATER association with anal atresia, vertebral anomalies and renal anomalies. He was operated due to anal atresia during the new-born period. Evaluation for the vertebral anomalies demonstrated sacral dysgenesis, coccyx agenesis and spina bifida at the C7 level. He was admitted to pediatric surgery with encopresis but on examination. He had hypertension. His abdominal ultrasonography demonstrates unilateral hydroureteronephrosis. Intravenous pyelography, DMSA and DTPA examinations revealed as non-functional right kidney. Right ureterovesical obstruction was demonstrated with cystoscopy. Nephrectomy had done because of his blood pressure levels were irregular. Clinical spectrum of the VATER association is variable. If each of the component of this association detect, renal malformations must be evaluated carefully.

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